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Reactivity | Human Mouse Rat |
Tested applications | WB IHC ICC IF FC |
Recommended Dilution | WB 1:500 - 1:2000 IHC 1:50 - 1:200 ICC 1:50 - 1:200 IF 1:50 - 1:100 FC 1:20 - 1:50 |
Calculated MW | 53 kDa |
Observed MW | Refer to figures |
Immunogen | Recombinant protein of human DES |
Storage Buffer | Store at -20℃. Avoid freeze / thaw cycles. Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
Synonym | CSM1; CSM2; LGMD2R; |
Immunohistochemistry of paraffin-embedded mouse skeletal muscle using DES antibody at dilution of 1:100 (40x lens).
Immunohistochemistry of paraffin-embedded human uterus using DES antibody at dilution of 1:100 (40x lens).
Immunohistochemistry of paraffin-embedded mouse heart using DES antibody at dilution of 1:100 (40x lens).
Immunohistochemistry of paraffin-embedded mouse bladder using DES antibody at dilution of 1:100 (40x lens).
Immunofluorescence
This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies.
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