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Reactivity | Human Mouse Rat |
Tested applications | WB IHC IF |
Recommended Dilution | WB 1:500 - 1:2000 IHC 1:50 - 1:200 IF 1:50 - 1:200 |
Calculated MW | 83kDa |
Observed MW | Refer to Figures |
Immunogen | Recombinant protein of human HADHA |
Storage Buffer | Store at -20℃. Avoid freeze / thaw cycles. Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
Synonym | GBP; ECHA; HADH; LCEH; MTPA; LCHAD; TP-ALPHA; |
Western blot analysis of extracts of various cell lines, using HADHA antibody.
Immunohistochemistry of paraffin-embedded human liver cancer using HADHA antibody at dilution of 1:100 (x40 lens).
Immunohistochemistry of paraffin-embedded human esophageal cancer using HADHA antibody at dilution of 1:100 (x40 lens).
Immunofluorescence analysis of U2OS cell using HADHA antibody. Blue: DAPI for nuclear staining.
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.
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